Dyssynergia cerebellaris myoclonica

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Dyssynergia cerebellaris myoclonica (Ramsey Hunt syndrome, myoclonus and ataxia, Spinodenate atrophy) is an an autosomal recessive or spontaneous condition characterised by:

It has childhood onset in the range 6 to 15 years (mean 10.4 years)[1]. There is some controversy as to how useful the label is as it does not appear to describe one pathological entity[2]. Recent classifications exclude: